Cystic fibrosis ndi matenda obadwa nawo omwe amakhudza machitidwe onse a thupi la munthu omwe amachititsa ntchentche-kupuma, kupweteka kwa thupi, kugonana, glands la thukuta. Matendawa ndi ofala, koma mpaka posachedwa, kufalikira kwa chithandizo chake sikunakopedwe. Odwala a Cystic fibrosis ayenera kulandira mankhwala osankhidwa bwino m'moyo wawo wonse, ayesetsedwe kawirikawiri ndi kuchitidwa nthawi yowonjezereka.
Chifukwa ndi mitundu ya cystic fibrosis
Chifukwa cha matendawa ndi kusinthika kwa jini yotchedwa fibrousis. Geni anapezedwa kokha zaka makumi atatu zapitazo. Kusintha kwa jini uku kumapangitsa kuti chinsinsi chobisika ndi glands chikhale cholimba kwambiri. Chinsinsi chobisika chimasinthasintha m'magazi ndi minofu, imayambitsa tizilombo toyambitsa matenda - nthawi zambiri Pseudomonas aeruginosa, Staphylococcus aureus, ndodo yamphongo. Zotsatira zake, kutukumula kosapitirira kumachitika.
Cystic fibrosis imapezeka mu mitundu itatu:
- pulmonary;
- matumbo;
- zosakaniza.
Zizindikiro za cystic fibrosis mwa ana obadwa kumene
- Kutsekeka m'mimba (mekonial ileus) - m'mimba mwachinyamatako kumwa madzi, sodium ndi klorini zimasokonezeka, chifukwa zimakhala ndi meconium. Mimba imakula mu mwana, imalira ndi bile, khungu limakhala louma ndi lopsa, minofu imapezeka pamimba, mwana amakhala wouma komanso wosachita, zizindikiro za poizoni zimadziwika ndi ana a ng'ombe
- Jaundice yaitali - amawonetseredwa pa theka la milandu ya leus, koma amatumikira ngati chizindikiro chodziimira pa matendawa. Zimatuluka chifukwa bile imakhala yandiweyani ndipo imatuluka kunja kwa ndulu.
- Mwanayo amathira makristasi amchere pa khungu la nkhope ndi pamphuno, khungu limakhala kukoma kwa mchere.
Zizindikiro za cystic fibrosis m'makanda
Kawirikawiri, cystic fibrosis imaonekera pamene khanda limasamutsira ku zakudya zophatikizana kapena jekeseni ndi zakudya zowonjezera:
1. Mpando umakhala wandiweyani, mafuta, wochuluka komanso wokhumudwitsa.
2. Chiwindi chakulitsidwa.
3. Pangakhale phokoso la rectum.
4. Mwanayo amatha kumbuyo mwakukula ndikukula zizindikiro za kupweteka kwa thupi:
- khungu limakhala louma ndi nthaka;
- amawonjezera ndi kuwononga thorax;
- mimba imakhala yayikulu ndi yotupa;
- Manja ndi miyendo imakhala yopyapyala ndi zolemba zala zapangidwe ngati "zotsekemera."
5. Kuchepetsa mwana wodwala kumayamba kutaya nthawi yaitali. Nkhono zowonongeka zimayambira mu bronchi ndipo zimalepheretsa kupuma bwinobwino. Mu ntchentche yambiri, mabakiteriya amakula molimbika, chifukwa cha kutupa kwa purulent.
Ana omwe ali ndi cystic fibrosis ayenera kulandira chithandizo chabwino. Zambiri zochiritsira zikuphatikizapo:
- Thandizo la antibacterial - kulimbana ndi matenda mu njira yopuma;
- mankhwala osokoneza bongo - kupweteka kwa sputum;
- Kinesitherapy - Kuchita kupuma kwapadera;
- hepatoprotectors - chifukwa cha liquefaction ya bile;
- Vitamini thérapies - kubwezeretsa imfa ya mavitamini ndi chitseko.
Kuwonetsa ana obadwa kwa cystic fibrosis
Cystic fibrosis ingapezeke chifukwa cha kuyeza kwa odwala ndi ma laboratory. Kuti matendawa azindikire mwamsanga, cystic fibrosis ikuphatikizidwa pulogalamu yoonetsera ana obadwa ndi matenda obadwa nawo komanso obadwa nawo.
Kuwonetsa mwana akadali kuchipatala kudzatenga chitsanzo cha magazi (nthawi zambiri chidendene) ndi njira yowuma. Izi zimachitika pa tsiku 4 mwa ana obadwa nthawi kapena tsiku la 7 m'mwana asanakwane. Chitsanzo cha magazi chimagwiritsidwa ntchito pamzere woyesera, womwe umayikidwa pansi pa phunziro la laboratory. Ngati pali kukayikira kwa cystic fibrosis, makolo amadziwitsidwa mofulumira za kufunikira kwa kufufuza kwina.