Matenda a Werlhof - thrombocytopenic purpura - matenda omwe amawoneka ngati amadzimadzimadzimadzimadzi omwe amachititsa kuti magazi asapitirire. Mankhwala opangidwa ndi tizilombo toyambitsa matenda amavala zowonjezera mitsempha yaing'ono. Kuphatikiza apo, pali kusungunuka kwa maselo a magazi ndi kuchepa kwa chiwerengero cha mapaleti.
Zifukwa za Matenda a Werlhof
Pakali pano, zomwe zimayambitsa thrombocytopenic purpura sizidziwika. Apatseni mitundu yoyamba ndi yachiwiri ya matenda a Verlhof. Mafomu apamtundu ndizobadwa mwachibadwa kapena amawonetsa chifukwa cha matenda opatsirana. Mafomu apakati ali ndi zizindikiro za matenda ambiri.
Zizindikiro za matenda a Verlhof
Nthendayi imayambira mwamphamvu, chifukwa palibe chifukwa chomveka, nthawi zina kutsutsana ndi matenda a m'mimba kapena ARI. Mmodzi wodwalayo ali pachigawo choyambirira, zizindikiro zotsatirazi zikuwonekera:
- malungo;
- kunyoza (kusanza kotheka);
- mutu;
- kufooka kwakukulu, kutopa;
- ululu m'chifuwa ndi mimba.
Chizindikiro chachikulu ndi mikwingwirima komanso mankhwala osokoneza bongo, omwe amatanthauzira dzina lachiwiri la thrombocytopenic purpura.
Patangotha kanthawi kochepa, matenda otsekula m'mimba amadziwika makamaka ngati:
- minofu, m'mimba m'magazi, komanso mwa akazi komanso uterine;
- mimba yamagazi , mucous membrane;
- Kutaya magazi mu retina wa diso;
- hemoptysis.
Mawonetseredwe achimake amatsatizana ndi matenda a ubongo, monga:
- kuchepetsa;
- kugona;
- kusokonezeka mu danga ndi nthawi;
- kuchepetsa masomphenya;
- osagwirizana.
Pa milandu yovuta, n'zotheka kukhala ndi coma.
Kuchepetsa pansi pa khungu kumakhala kwakukulu ndipo kumakhala malo ambiri. Malinga ndi mankhwalawa, mafinya amakhala ndi mtundu wofiira-bulauni kapena wachikasu (monga kuvulaza kokalamba).
Kuzindikira kwa matenda a Verlhof kumayamba ndi kukayezetsa wodwalayo ndi anamnesis. Kuvuta kwa matendawa kumaphatikizapo mayesero awa:
- Kusanthula kwakukulu kwa magazi (OAK). Matendawa amatsimikiziridwa mwa kuchepetsa mlingo wa erythrocyte ndi hemoglobini, kuchepetsa chiwerengero cha mapuloleteni ndikupeza antiplatelet antibodies.
- Mphepete mwazengereza - kutenga fupa la fupa kuti lifufuze pogwiritsa ntchito sternum puncture. Phunziro la maselo a selo, kuwonjezeka kwa nambala ya megakaryocytes, chiwerengero chochepa cha mapaleleteni, amapezeka, pamene palibe kusintha kwina m'mafupa, mwachitsanzo, zomwe zimakhala ndi maonekedwe a zotupa.
- Trepanobiopsy - kufufuza mafupa a periosteum ndi fupa (kuchokera kumtunda wa chiuno), atatengedwa ndi chithandizo cha mankhwala a trephine. Ndili ndi matenda a Verlhof, chiŵerengero cha mafuta ndi mafuta a mafupa amtundu wa mafupa amatsatana ndi chizoloŵezi.
Kuchiza kwa Matenda a Verlhof
Njira zothandizira zimadalira nthawi ya matendawa. Chithandizo chikuchitika ndi njira imodzi zotsatirazi:
- Kugwiritsiridwa ntchito kwa corticosteroids pofuna kumanga matenda a chiwindi ndi kuonjezera mlingo wa mapulogalamu m'magazi. Prednisalon amalamulidwa pa mlingo wa 1 mg pa 1 makilogalamu a kulemera kwa thupi tsiku lililonse. Ngati matendawa ali aakulu, mlingowo umapitirira kawiri.
- Ngati zotsatira zake sizingatheke, wodwalayo akulimbikitsidwa kuchotsa nthata . Malinga ndi chiwerengero cha zachipatala, 80% mwa odwala pambuyo pochita opaleshoni amachira bwinobwino.
- Nthawi zambiri, pambuyo pa spleenectomy, kutuluka kwa magazi, ndipo matendawa amakhalabe, ma immunosuppressants amalembedwa (Azathioprine, Vincristine) ndi glucocosteroids.
Kuchotsa zizindikiro zakunja za matenda a hemorrhagic, haemostatic mawotchi amagwiritsidwa ntchito:
- Adroxoni;
- Zakudya;
- Siponji ya Hemostatic;
- estrogens.