Matupi a Ketone mumtsuko - zifukwa ndi chithandizo cha ketonuria

Thupi la Ketone mu mkodzo ndi chizindikiro chowopsya, chosonyeza kuti kuwonongeka kwakukulu kwachitika mu ntchito ya thupi. Tiyenera nthawi yomweyo kupeza thandizo lachipatala ndikutsatira malangizo a dokotala mosalephera. Vutoli silingalephereke, chifukwa zotsatira zake zingakhale zoopsa.

Matupi a Ketone mumtsuko - izi zikutanthauza chiyani?

Gululi la zinthu zimagwirizanitsa zinthu zingapo: acetoacetic ndi beta-hydroxybutyric acids, acetone. Ndiwo zinthu zakuthupi za kuwonongeka. Komabe, ngati zotsatira za mayesero a wodwala adokotala akuwona kukhalapo kwa zinthu izi, adzapitiriza kufufuza ndikupereka chithandizocho. Pachifukwa ichi ndizomveka kukhala ndi chidwi ndi zomwe ketone thupi mumthambo limatanthauza. Zizindikiro zoterezi zikhoza kumveka zambiri.

Kodi thupi la ketone ndi liti?

Zinthu zimenezi zimagwiritsidwa ntchito ngati mankhwala a metabolism omwe amapangidwa pachiwindi. Amaoneka panthawi imene mafuta akuwonongeka, komanso pakupanga shuga. Ngati thupi limagwira ntchito bwino, ketoni mu mkodzo sichipezeka. Zimachotsedwa kwathunthu, zimagawanika m'madzi ndi carbon dioxide. Acetonuria (aka ketonuria) ndipamwamba kwambiri m'mikodzo ya zinthu zoterezi. Matendawa amapezeka kwa akulu ndi ana.

Matenda a Ketone mumtsuko - nthawi zambiri

Tsiku lirilonse kuchokera mu thupi la munthu wamkulu yemwe ali ndi mkodzo, mpaka 50 mg ya acetone zinthu zimatulutsidwa. Pamene mankhwalawa amachoka, sangathe kudziwika ndi njira za laboratory. Mu mawonekedwe ndi zotsatira za maphunziro a zachipatala, chizindikiro cha KET chimagwiritsidwa ntchito kutchula matupi a ketone. Kawirikawiri zokhutira zawo zili pakati pa 0 ndi 0.05 mmol / l. Zochitika zotere za thupi la ketone mu mkodzo zimaonedwa kuti ndi zosayenerera. Ndi zotsatira izi, thupi limagwira ntchito bwino.

Ketonuria - Zimayambitsa

Pomwe thupi limagwira ntchito, thupi la munthu limalandira mphamvu kuchokera ku shuga komanso kusungira chiwindi. Izi ndi zokwanira kuti agwire ntchito pamodzi. Komabe, pali zifukwa zambiri pamene thupi lawonjezera mphamvu yogwiritsira ntchito mphamvu. Panthawiyi, malo ogulitsira glycogen amatha, ndipo thupi limayamba kupanga maselo ake. Paziwalo zamagetsi zamtundu wa ketone zimapangidwa. "Zosowa" zawo zimachokera ku mkodzo.

Ngati matupi a ketone amapezeka mkodzo, zifukwa izi zingakhale motere:

Ketonuria mu matenda a shuga

Kukula kwa matenda oterewa kumachepetsa kuchepa kwa shuga m'magazi. Chifukwa chake, thupi limakumana ndi kusowa kwakukulu. Izi zimachitika ngati mlingo wa insulini wosankhidwa bwino. Komabe, ketonuria mu mtundu wachiwiri wa shuga amachitanso. Izi zimachokera kukumwa kwa zakudya zakuda kwambiri kapena njala yautali.

Ketonuria ali ndi pakati

Chiwalo cha mayi woyembekezera chimakhala ndi katundu wolemetsa. Nthaŵi zonse samakhala ndi nthawi yosintha mofulumira kusintha komwe kumachitika mkati mwake. M'miyezi yoyamba ya mimba, kuwonjezeka kwa matupi a ketone mu mkodzo wa amayi ndi zosachitika kawirikawiri. Ndili ndi vuto lomwe amayi ambiri amakumana nawo, kuyambira sabata lachisanu ndi chiwiri. Komabe, ngakhale panthaŵiyi, ndi kuwonjezeka pang'ono kwa chizindikiro ichi, mimba ikhoza kuonedwa ngati yachilendo. Ngati acetone mu mkodzo yawonjezeka kwambiri, zifukwa izi zingakhale motere:

Ngati matupi a ketone mumkodzo wa mayi wapakati ali pamwamba, muyenera kuchita mwamsanga. Pankhaniyi, mayi ndi mayi omwe ali m'tsogolo ali pangozi. Ngati palibe chithandizo chamankhwala nthawi yake, mavuto ngati amenewa angakhalepo:

Ketonuria - Zizindikiro

Pa chitukuko cha acetonuria, magawo atatu ndi osiyana, omwe ali ndi chithunzi chake cha kuchipatala. Fomu yofewa imaphatikizapo zizindikiro zotsatirazi:

Chikhalidwe cha mawonekedwe apakati chimakhala ndi zizindikiro:

Maonekedwe akuluakulu a acetonuria amadziwika ndi zizindikiro zotere:

Kutsimikiza kwa thupi la ketone mu mkodzo

Zizindikiro zomwe zimagwirizana ndi acetonuria, zithandizani pa nthawi yake kuti muzimva phokoso. Komabe, n'zotheka kupeza thupi la ketone mumkodzo pokhapokha atathandizidwa ndi kusanthula kwapadera. Zonse zachitika kuchipatala, choncho kunyumba. Ndipo m'nthawi yoyamba, komanso pa yachiwiri, ngati mutapeza zotsatira zabwino, muyenera kumalankhula ndi dokotala nthawi yomweyo. Kuteteza ketonuria kuyenera kupatsidwa kwa dokotala wodziwa bwino. Zomwe mungayankhe kwa dokotala - zimadalira mbali za acetonuria:

Kusinkhasinkha kwa mitsempha kwa matupi a ketone

Mu ma laboratory, acetone mu mkodzo amapezeka pogwiritsa ntchito chitsanzo chapadera. Zotsatira zimatanthauzidwa motere:

Kuti mudziwe kukhalapo kwa matupi a ketone mu mkodzo, zofunikira zowonongeka ziyenera kukololedwa bwino. Mungathe kuchita izi motere:

  1. Mmawa wodwala ayenera kutsukidwa bwino.
  2. Zakudya zamagetsi (mlingo 70-100 ml) ziyenera kusonkhanitsidwa mu chidebe chopanda kanthu ndipo nthawi yomweyo chimaphimbidwa ndi chivindikiro.
  3. Mitsempha iyenera kubweretsedwa ku labotale ikadali yotentha.

Kutsimikiza kwa thupi la ketone mu mkodzo ndi mayesero oyesa

Njirayi ikugwiritsidwa ntchito pakhomo. Mapepala oyesa kuyesa acetone mu mkodzo akhoza kugulitsidwa pa pharmacy iliyonse popanda mankhwala. Mfundo ya njirayi ndi yakuti pamene acetone ikukhudzana ndi reagent, ziwonetsero zamakono. Mungathe kudziwa zotsatira zake poyerekeza mtundu wa mndandanda wa mayeso ku acetone mu mkodzo ndi msinkhu. Kuti muyese khalidwe lofufuza, muyenera kutsatira zotsatirazi:

  1. Pezani chidutswa chimodzi kuchokera mu chubu.
  2. Yesetsani kuyesa kwa masekondi pang'ono mu chidebe ndi mkodzo watsopano.
  3. Sungani mosamala madzi owonjezera podutsa pamphepete mwa mbale ndi mkodzo.
  4. Sintha zotsatira.
  5. Ngati zotsatirazo ziri zabwino, muyenera kupeza chithandizo chamankhwala.

Ketonuria - mankhwala

Mankhwala opatsirana matendawa amachepetsedwa kukhala acetone m'thupi. Izi zikhoza kupindula mwa kuonetsetsa kuti madzi akuyendera bwino. Imwani kawirikawiri (maminiti khumi ndi khumi ndi awiri mphambu khumi ndi awiri mphambu khumi ndi zisanu ndi zisanu ndi zitatu) muzipinda zazing'ono. Njira yabwino ndi madzi a alkaline opanda carbonated ndi decoction wa zoumba. Pofuna kuchepetsa matupi a ketone kuchipatala, mankhwala opatsirana amatha kupangidwa ndi mankhwala a saline.

Kuyeretsa thupi kumathandizira zotsatirazi:

Mitsempha ya mumtambo ikukwera ndipo vutoli likuphatikizidwa ndi kusanza, jekeseni wamakono angapangidwe. Wodwalayo ayenera kusiya kudya tsiku limenelo. Pa nthawi imodzimodziyo, nkofunika kusamalira kuchepetsa katundu pachiwindi, chimene sichikugwirizana ndi kukonza matupi a ketone. Kukhazikitsa ntchito ya thupi ili mkati kungathandize mankhwala oterowo:

Monga chithandizo chothandizira chingakonzedwe mankhwala ochiritsira. Monga mankhwala osokoneza bongo, nthawi zambiri amagwiritsidwa ntchito pogwiritsira ntchito mankhwala osokoneza bongo, mwachitsanzo, kuchokera ku hawthorn kapena valerian. Kuchotsa mowa kumathandizira tiyi ya chamomile, zakumwa za zipatso za mabulosi ndi zipatso za zouma. Komanso, panyumba, mukhoza kupanga enema (kuyeretsa madzi okwanira 1 litani supuni 1 ya mchere).

Kudya ketonuria

Yolani mkhalidwe wa wodwalayo ndikuletsa kuwonjezeka kwina kwa acetone kungakhale kudzera mwa zakudya zabwino. Zakudyazi ziyenera kuperekedwa ndi dokotala yemwe akupezekapo. Pofuna kupanga zakudya, adzalingalira zomwe zimayambitsa kuchuluka kwa ketoni mu mkodzo, komanso momwe wodwala alili. Zakudyazi ndizovuta kwambiri ndipo ziyenera kuwonetsedwa mwatsatanetsatane. Zamakina zotengera ketonuria:

Analimbikitsa kudya ndi ndondomeko yapamwamba mu mkodzo wa matupi a ketone: