Scleroderma - zizindikiro

Scleroderma ndi matenda a khungu kumene ziwiya zazing'ono zamoyo zonse zimakhudzidwa ndi kuwonongeka kwa iwo. Scleroderma ili ndi chikhalidwe chopita patsogolo, chomwe m'tsogolomu, popanda kuthandizidwa ndi thupi kumabweretsa mavuto omwe ali nawo olemala.

Mwamwayi, mankhwala amasiku ano satha kuthetsa matendawa, koma kuchotsedwa kwa zizindikiro kumathandiza kuti thupi likhale loyenera.

Ku America ndi ku Ulaya, lero akupanga maselo othandizira kuti athetse matendawa, koma panopa sakudziwika kuti ndi oyenera komanso oyenera. Zimadziwika kuti mu 93% mwa odwala omwe ali ndi scleroderma amamva mankhwala omwewo.

Scleroderma imatchula mtundu umodzi wa nyamakazi .

Zifukwa za Scleroderma

Mofanana ndi matenda ena ambiri omwe ali ovuta komanso otukuka, systemic scleroderma amaonedwa ngati majini. Komabe, ndizomveka kuzindikira kuti izi zikhoza kukhala chimodzi mwa zinthu zomwe zimalimbitsa mchitidwe wofanana wa thupi ndi zina zomwe sizikukondweretsa.

Kugwiritsa ntchito mankhwala osokoneza bongo kumawoneka kuti ndi omwe amachititsa kuti scleroderma iwonongeke. Zidazi zimatenthedwa, ndipo zimayandikana ndi ma collagen ndi fibrous tissue form. Makoma a zombozi amatha kugwira ntchitoyi, kutaya mphamvu, mpaka kutsekedwa kwathunthu kwa lumens.

Chikhalidwe ichi cha ziwiya chimayambitsa kuswa kwa magazi koyamba m'madera osiyana, ndiyeno mbali zonse za thupi ngakhale ziwalo za mkati. Komanso, izi zimayambitsa kuphwanya kwakukulu - mucosa ndi wochepa thupi, chifukwa cha zomwe, choyamba, mimba ndi mimba zimasautsika. Koma machitidwe ena a thupi ndi kutupa kwa mitsempha ya mitsempha ndi zovuta zapakati pafupipafupi zimakhala zowonongeka, zomwe zimaphatikizapo matenda aakulu mu thupi: chotupa chapakati mucosa sichilola kudya zakudya zachibadwa, mapapu amaphwanya mpweya wa carbon dioxide, ndi mitsempha ya minofu yafupika.

Choncho, matendawa amachititsa kuti zipatala zambiri zisagwire ntchito, zomwe zimakhala zovuta kuchiza madokotala.

Kuphatikiza pa hypothermia, matenda a mitsempha, mankhwala, matenda a chitetezo cha mthupi, komanso ngakhale nthawi zonse zotsatira za kugwedeza thupi panthawi yantchito zingapangitsenso scleroderma.

Zizindikiro za scleroderma

Pamene matendawa amapezeka katalatini khungu. Malingana ndi mawonetseredwe ake, scleroderma ili ndi mitundu yosiyanasiyana.

Limited scleroderma

Ndi mawonekedwe awa, zigawo zapamwamba za khungu zimakhudzidwa, ndipo ena onse samavutika. Mtundu umodzi wa scleroderma wa mtundu uwu ndi plaque scleroderma, momwe malo ang'onoang'ono okhala ndi mawonekedwe ozungulira amakhudzidwa. Choyamba, pali mawanga omwe ali ndi mtundu wa pinkish-violet, kenako zimayambira - zisindikizo, ndipo gawo lomalizira la kukula kwa scleroderma ndi atrophy.

Kuyamba kwa matenda ndi imperceptible - angapo mawanga kuonekera, kawirikawiri pa mkono. Ziri zazikulu - zazikulu kuposa chikhato cha dzanja lanu. Chinthu chodziwika bwino cha scleroderma ndi chakuti m'madera a mawanga amatha kutayika tsitsi. Nthawi yamapangidwe ikhoza kukhala ndi nthawi yayitali - zaka ndi miyezi, ndipo samawonetsa atrophy.

Juvenile scleroderma pankhaniyi ali ndi mawonetseredwe ofanana.

Akufalikira scleroderma

Mtundu uwu wa scleroderma umawonekera mowala kuposa mawonekedwe ochepa - chimfine cha munthu chimatuluka, kupweteka kwa miyendo ndi ntchentche pang'ono. Kenaka imayamba kuwonongeka kwa khungu konsekonse, komwe kuli ndi magawo atatu: kutupa kwa minofu, induration (compaction) imachitika, ndiyeno atrophy.

Mtundu wa khungu umakhala ndi chikasu chachikasu, ndipo mbali yosiyana ya mawonekedwe ameneĊµa ndi yakuti sangathe kupukutidwa. Ngati mumakanikiza pakhungu, dzenje silinapangidwe. Kwa munthu amene ali ndi matendawa, zimakhala zovuta kusunthira, ndipo nkhope imapeza mawonekedwe ngati mask.