Matenda a Marfan ndi matenda omwe safala kwambiri. Malingana ndi chiwerengero, matendawa amapezeka mwa munthu mmodzi pa 5,000. Nthawi zambiri, matendawa ndi olowa. Pa ma 75%, makolo amapatsira ana awo mankhwalawa.
Zomwe zimayambitsa Marfan's syndrome zimakhala kusintha kwa jini lomwe limayambitsa kapangidwe ka fibrilin. Ndizimenezi ndi mapuloteni ofunika kwambiri a thupi, omwe amachititsa kuti thupi likhale lopangidwa komanso likhale lolimba.
Wodziwika ndi Marfan syndrome pathological amasintha mu mtima, mitsempha ya mitsempha ndi minofu ya minofu. Chosowa chachikulu chiri mu matenda a collagen ndipo chimakhudza zotupa zowonongeka.
Zizindikiro za matendawa
Matenda a Marfan, zizindikiro zake zomwe zimawonetsedwa m'njira zosiyanasiyana, zimakula makamaka ndi ukalamba ndi ukalamba wa munthu. Koma mafupa a wodwalayo, ali ndi zotsatirazi:
- kukwera kwakukulu;
- mafupa osinthasintha ndi owonda;
- Manja ali ndi Marfan's syndrome, ngati miyendo, ali ndi zala zazikulu;
- nkhope yopapatiza yayitali;
- nthawi zambiri mano osagwirizana;
- Kusindikizidwa kapena convex sternum;
- chithandizo;
- mapafupi .
Odwala ambiri omwe ali ndi matendawa amavutika ndi myopia, cataracts kapena glaucoma. Chifukwa cha chilema mumatenda ofanana, nthawi zambiri anthu amadwala matenda aakulu a mtima. Nthawi zina zimayambitsa imfa mwadzidzidzi. Pamene matenda a Marfan amapezeka, mtima wa wodwalayo umakhala phokoso. Pali phokoso ndi mpweya wochepa.
Anthu omwe ali ndi matenda a Marfan ali ndi zofooka kapena zofooka m'milingo. Kawirikawiri amakhala ndi vuto la kupweteka kapena vuto la kupuma m'maloto. Kuopsa kwa khansa ya m'mapapo kumawonjezera kwambiri.
Chizindikiro Marfan, zomwe zizindikiro zake zimasiyana kwambiri, zimachepetsa moyo wa wodwalayo kufikira zaka 40-45.
Chizindikiro cha matendawa
Kuchita zamankhwala, ndi mwambo kusiyanitsa mitundu yambiri ya Marfan syndrome:
- chofotokozedwa;
- adachotsedwa.
Mphamvu ya kuuma ingakhale yovuta kapena yofatsa.
Malinga ndi momwe matendawa amachitira, amatha kukhala okhazikika kapena opitirira.
Zosokoneza
Poyamba, matendawa a Marfan syndrome amachokera pa kufufuza kwa pedigrees wodwalayo. Mmene thupi la munthu limagwirira ntchito komanso laumunthu limaphunziranso. Kugwirizana ndi kufanana kwa mbali iliyonse ya thupi kumafufuzidwa.
Monga lamulo, kuti matendawa ndi ofunika kuti akhale ndi chimodzi mwa zizindikiro zisanu zazikulu za matendawa:
- chithunzi;
- kusuntha kwa diso la diso;
- kyphoscoliosis;
- aortic aneurysm;
- kupunduka kwa sternum.
Pano pakhale pali zizindikiro zina ziwiri:
- mphukira ya mitral ;
- myopia;
- kukwera kwakukulu;
- pneumothorax;
- chiwonongeko;
- kusakanikirana kwa ziwalo;
- stria.
Kawirikawiri, matenda a matendawa sachititsa mavuto. Komabe, mu 10% za milandu zina zowonjezereka zogwiritsira ntchito X-ray zimayikidwa. Matenda a Marfan, omwe amadziwika kuti ndi olondola, nthawi zina akhoza kusokonezeka ndi matenda omwewo - Matenda a Lois-Datz. Njira zothandizira matenda ndi zosiyana, choncho ndizofunika kwambiri kuti musatenge matenda ena.
Njira Zothandizira
Kuti adziwe matenda oyenerera, wodwalayo ayenera kuyendera akatswiri ena:
- katswiri wa zamoyo;
- minofu;
- chibadwa;
- ophthalmologist.
Marfan's syndrome sichikugwirizana ndi mankhwala enaake. Izi ndi chifukwa chakuti asayansi sanaphunzire momwe angasinthire majini osinthika. Komabe, pali mitundu yambiri ya mankhwala omwe angapangidwe kuti apititse patsogolo machitidwe ndi chikhalidwe cha thupi linalake komanso kupeĊµa mavuto.
Ndikofunika kutsatira ndondomeko yoyenera, kudya mavitamini komanso kukhala ndi moyo wathanzi. Matenda a Marfan, amene mankhwala ake ndi ovuta, amafuna kuti wodwala achite zovuta zozizwitsa. Komabe, katunduyo ayenera kukhala wodekha ndi wosasamala.